Sensorineural deafness
Nerve deafness; Hearing loss - sensorineural; Acquired hearing loss; SNHL; Noise-induced hearing loss; NIHL; Presbycusis
Sensorineural deafness is a type of hearing loss. It occurs from damage to the inner ear, the nerve that runs from the ear to the brain (auditory nerve), or the brain.
Considerations
Symptoms may include:
- Some sounds seem too loud.
- You have problems following conversations when two or more people are talking.
- You have problems hearing in noisy areas.
- It is easier to hear men's voices than women's voices.
- It is hard to tell high-pitched sounds (such as "s" or "th") from one another.
- Other people's voices sound mumbled or slurred.
- You have problems hearing when there is background noise.
Other symptoms include:
-
Feeling of being off-balance or dizzy (more common with
Meniere disease
and
acoustic neuromas
)
Meniere disease
Ménière disease is an inner ear disorder that affects balance and hearing.
Acoustic neuromas
An acoustic neuroma is a slow-growing tumor of the nerve that connects the ear to the brain. This nerve is called the vestibular cochlear nerve. It...
-
Ringing or buzzing sound in the ears (
tinnitus
)
Tinnitus
Tinnitus is the medical term for "hearing" noises in your ears. It occurs when there is no outside source of the sounds. Tinnitus is often called "r...
Causes
The inner part of the ear contains tiny hair cells (nerve endings), that change sounds into electric signals. The nerves then carry these signals to the brain.
Sensorineural hearing loss (SNHL) is caused by damage to these special cells, or to the nerve fibers in the inner ear. Sometimes, the hearing loss is caused by damage to the nerve that carries the signals to the brain.
Sensorineural deafness that is present at birth (congenital) is most often due to:
- Genetic syndromes
-
Infections that the mother passes to her baby in the womb (
toxoplasmosis
,
rubella
,
herpes
)
Toxoplasmosis
Congenital toxoplasmosis is a group of symptoms that occur when an unborn baby (fetus) is infected with the parasite Toxoplasma gondii.
Rubella
Congenital rubella is a condition that occurs in an infant whose mother is infected with the virus that causes German measles. Congenital means the ...
Herpes
Newborn infants can become infected with herpes virus during pregnancy, during labor or delivery, or after birth.
Sensorineural hearing loss may develop in children or adults later in life (acquired) as a result of:
-
Age-related hearing loss
Age-related hearing loss
Age-related hearing loss, or presbycusis, is the slow loss of hearing that occurs as people get older.
- Disease of the blood vessels
- Immune disease
-
Infections, such as
meningitis
,
mumps
,
scarlet fever
, and
measles
Meningitis
Meningitis is an infection of the membranes covering the brain and spinal cord. This covering is called the meninges.
Mumps
Mumps is a contagious disease that leads to painful swelling of the salivary glands. The salivary glands produce saliva, a liquid that moistens food...
Scarlet fever
Scarlet fever is caused by an infection with bacteria called A streptococcus. This is the same bacteria that cause strep throat.
Measles
Measles is a very contagious (easily spread) illness caused by a virus.
- Injury
-
Loud noises or sounds, or
loud sounds that last for a long time
Loud sounds that last for a long time
Occupational hearing loss is damage to the inner ear from noise or vibrations due to certain types of jobs.
-
Meniere disease
Meniere disease
Ménière disease is an inner ear disorder that affects balance and hearing.
- Tumor, such as acoustic neuroma
- Use of certain medicines
- Working around loud noises every day
In some cases, the cause is unknown.
What to Expect at Your Office Visit
The goal of treatment is to improve your hearing. The following may be helpful:
- Hearing aids
- Telephone amplifiers and other assistive devices
- Sign language (for those with severe hearing loss)
- Speech reading (such as lip reading and using visual cues to aid communication)
A cochlear implant may be recommended for certain people with very severe hearing loss. Surgery is done to place the implant. The implant makes sounds seem louder, but does not restore normal hearing.
Cochlear implant
A cochlear implant is a small electronic device that helps people hear. It can be used for people who are deaf or very hard of hearing. A cochlear ...
You will also learn strategies for living with hearing loss and advice to share with those around you for talking to someone with hearing loss .
Living with hearing loss
No definition available for this article.
Talking to someone with hearing loss
It may be hard for a person with hearing loss to understand a conversation with another person. Being in a group conversation can be even harder. T...
References
Arts HA. Sensorineural hearing loss in adults. In: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Head & Neck Surgery . 6th ed. Philadelphia, PA: Elsevier Saunders; 2015:chap 150.
Lonsbury-Martin BL, Martin GK. Noise-induced hearing loss. In: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Head & Neck Surgery . 6th ed. Philadelphia, PA: Elsevier Saunders; 2015:chap 152.
National Institute on Deafness and Other Communication Disorders. Noise-induced hearing loss. NIH Pub. No. 14-4233. Updated May 15, 2015. www.nidcd.nih.gov/health/noise-induced-hearing-loss . Accessed June 28, 2016.
Shibata SB, Shearer AE, Smith RJH. Genetic sensorineural hearing loss. In: Flint PW, Haughey BH, Lund V, et al, eds. Cummings Otolaryngology: Head & Neck Surgery . 6th ed. Philadelphia, PA: Elsevier Saunders; 2015:chap 148.
-
Ear anatomy - illustration
The ear consists of external, middle, and inner structures. The eardrum and the 3 tiny bones conduct sound from the eardrum to the cochlea.
Ear anatomy
illustration
Review Date: 5/25/2016
Reviewed By: Sumana Jothi, MD, specialist in laryngology, Assistant Clinical Professor, UCSF Otolaryngology, NCHCS VA, SFVA, San Francisco, CA. Review provided by VeriMed Healthcare Network. Also reviewed by David Zieve, MD, MHA, Isla Ogilvie, PhD, and the A.D.A.M. Editorial team.